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The global frequency of galactosemia is estimated at approximately one in every 62,000 live births; in the USA a recent prevalence of one in 30,000 to one in 60,000 live births have been reported (Pyhtila, 2015). Across Europe, incidence varies greatly (Morel-Garcia, 2014), with a much lower frequency reported in Asian populations (Choi, 2014). However, now in the Philippines occurring to one in 310,694 live births (Padilla et al., 2014). The seriousness of galactosemia cannot be underscored that nurses primarily must come to grips with this life-threatening disease. Recognizing the clear possibility and actual incidences of galactosemia in the Philippines, this study aimed to assess the level of knowledge of management of this disorder among selected staff nurses of GTLMH and nursing students of MSU-IIT in consideration of their demographic profile, an assessment of their level of knowledge of management, and the relationship between these two variables. Using the descriptive-correlational-comparative research design, random sampling, and standardized questionnaire which was subjected to a pilot study, yielded a Cronbach alpha of 85.12% indicating a high level of internal consistency. Then, the results revealed (1) majority of the respondents have good level of knowledge on general galactosemia knowledge and diet & lifestyle, and an average level of knowledge on signs & symptoms and medication & management, (2) Pearson Correlation Coefficient showed a low direct relationship of the respondents when grouped according to their demographic profile: age (R: -0.00739) which indicated the higher the age of the respondents, the lower the level of knowledge of management concerning galactosemia, and educational attainment (R: 0.03687) which indicated the higher the educational attainment, the higher the level of knowledge of management of galactosemia. Hence, despite the staff nurses having no leverage/advantage over the nursing students, it is imperative to increase the knowledge, more focused seminars and workshops among nurses concerning galactosemia and newborn screening.